Cervicovaginal Agenesis: A Case Report of a Rare Congenital Anomaly with Delayed Clinical Recognition    : A Case Report of Cervicovaginal Agenesis

Nawazish Ali; Umm E Aiman Saleem; Rida Asghar; Aqsa Aman; Rakhshinda Inam; Mohammad Osama; Muneeba Attique

doi:10.54393/pbmj.v9i1.1335

Authors

Nawazish Ali Gomal Medical College, Dera Ismail Khan, Pakistan
Umm E Aiman Saleem Gomal Medical College, Dera Ismail Khan, Pakistan
Rida Asghar Department of Gynaecology and Obstetrics, Gomal Medical College, Dera Ismail Khan, Pakistan
Aqsa Aman Department of Gynaecology and Obstetrics, Gomal Medical College, Dera Ismail Khan, Pakistan
Rakhshinda Inam Department of Gynaecology and Obstetrics, Gomal Medical College, Dera Ismail Khan, Pakistan
Mohammad Osama Gomal Medical College, Dera Ismail Khan, Pakistan
Muneeba Attique Gomal Medical College, Dera Ismail Khan, Pakistan

DOI:

https://doi.org/10.54393/pbmj.v9i1.1335

Keywords:

Premenarchial, Hematometra, Cervical Agenesis, Uterovaginal Anastomosis, Case Report

Abstract

Rare congenital Mullerian anomalies include cervical agenesis. It has been found in 39% of cervical agenesis instances, which makes its association with vaginal agenesis which occurs even less frequently much rarer. For this ailment, a hysterectomy was the standard of care. However, due to improvements in assisted reproductive techniques and surgical advancements, conservative surgery can now be considered the first-line therapy Patients with primary amenorrhea should be actively evaluated for underlying causes. cervicovaginal agenesis is uncommon and has a variety of presentations. In a successful case of cervicovaginal agenesis treated with cervicovaginoplasty, a 14-year-old adolescent girl who had been experiencing cyclical pelvic discomfort and primary amenorrhea for five months came to the Women and Children Hospital Dera Ismail Khan's outpatient department. The patient's menstrual periods returned after surgery, and her cyclical abdominal pain decreased. Patients with primary amenorrhea should be actively evaluated for underlying causes. cervicovaginal agenesis is uncommon and has a variety of presentations. This might cause misdiagnosis and treatment delays. it is important to establish early diagnosis and proper management of these surgically amenable lesions to preserve normal physiology and fertility and prevent complications.

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